FITC标记的腺苷单磷酸脱氨酶1抗体
产品名称： FITC标记的腺苷单磷酸脱氨酶1抗体
英文名称： Anti-AMPD1/FITC
产品编号： HZ-2077R-FITC
产品价格： null
产品产地： 中国/上海
品牌商标： HZbscience
更新时间： 2023-08-17T10:24:20
使用范围： IF=1:50-200
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Rabbit Anti-AMPD1/FITC Conjugated antibody
FITC标记的腺苷单磷酸脱氨酶1抗体
| 英文名称 | Anti-AMPD1/FITC |
| 中文名称 | FITC标记的腺苷单磷酸脱氨酶1抗体 |
| 别 名 | AMPD1; AMPD-1; AMPD1; AMPD-1; Adenosine monophosphate deaminase 1 (isoform M); Adenosine monophosphate deaminase 1; AMP deaminase 1; AMP deaminase isoform M; AMPD 1; Ampd01; MAD; MADA; Myoadenylate deaminase; RATAMPD01; AMPD1_MOUSE. |
| 规格价格 | 100ul/2980元 购买 大包装/询价 |
| 说 明 书 | 100ul |
| 研究领域 | 细胞生物 信号转导 激酶和磷酸酶 |
| 抗体来源 | Rabbit |
| 克隆类型 | Polyclonal |
| 交叉反应 | Human, Mouse, Rat, Dog, Cow, Horse, Sheep, |
| 产品应用 | IF=1:50-200 not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
| 分 子 量 | 86kDa |
| 性 状 | Lyophilized or Liquid |
| 浓 度 | 1mg/ml |
| 免 疫 原 | KLH conjugated synthetic peptide derived from mouse AMP deaminase 1 (125-175aa) |
| 亚 型 | IgG |
| 纯化方法 | affinity purified by Protein A |
| 储 存 液 | 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
| 保存条件 | Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. |
| 产品介绍 | background: AMP deaminase (AMPD) is an allosteric enzyme that plays a critical role in energy metabolism. There are three functional isoforms of AMPD. AMPD1 is the skeletal muscle-specific isoform M located in type II muscle fibers, neuromuscular junctions and in capillaries. Defects in AMPD1 are the cause of adenosine monophosphate deaminase deficiency muscle type (AMPDDM). AMPDDM is a metabolic disorder resulting in exercise-related myopathy. It is characterized by exercise-induced muscle aches, cramps, and early fatigue. Function: AMP deaminase plays a critical role in energy metabolism. Subunit: Homotetramer Similarity: Belongs to the adenosine and AMP deaminases family. Database links: Entrez Gene: 270 Human Entrez Gene: 229665 Mouse Entrez Gene: 25028 Rat Omim: 102770 Human SwissProt: P23109 Human SwissProt: Q3V1D3 Mouse SwissProt: P10759 Rat Unigene: 89570 Human Unigene: 331272 Mouse Unigene: 9794 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic application |
AMP-脱氨酶（AMPD）是一种在能量代谢中起关键作用的变构酶。AMPD有三种功能性亚型。AMPD1是骨骼肌特异性的亚型M，位于II型肌纤维、神经肌肉接头和毛细血管中。AMPD1的缺陷是腺苷一磷酸脱氨酶缺乏型肌肉（AMPDDM）的原因。AMPDDM是一种代谢紊乱，导致运动相关肌病。它的特点是运动引起的肌肉疼痛，抽筋，和早期疲劳。